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5. HEADACHE ATTRIBUTED TO HEAD AND/OR NECK TRAUMA 6. HEADACHE ATTRIBUTED TO CRANIAL OR CERVICAL VASCULAR DISORDER 6.1. Headache attributed to ischaemic stroke or transient ischaemic attack6.2. Headache attributed to non-traumatic intracranial haemorrhage [I62] 6.3. Headache attributed to unruptured vascular malformation [Q28] 6.3.1. Headache attributed to saccular aneurysm [Q28.3] 6.3.2. Headache attributed to arteriovenous malformation (AVM) [Q28.2] 6.3.3. Headache attributed to dural arterio-venous fistula [I67.1]6.3.4. Headache attributed to cavernous angioma [D18.0]6.3.5. Headache attributed to encephalotrigeminal or leptomeningeal angiomatosis (Sturge Weber syndrome) [Q85.8]6.4. Headache attributed to arteritis [M31]6.5. Carotid or vertebral artery pain [I63.0, I63.2, I65.0, I65.2 or I67.0]6.6. Headache attributed to cerebral venous thrombosis (CVT) [I63.6] 6.7. Headache attributed to other intracranial vascular disorderBibliography7. HEADACHE ATTRIBUTED TO NON-VASCULAR INTRACRANIAL DISORDER 8. HEADACHE ATTRIBUTED TO A SUBSTANCE OR ITS WITHDRAWAL 9. HEADACHE ATTRIBUTED TO INFECTION 10. HEADACHE ATTRIBUTED TO DISORDER OF HOMOEOSTASIS 11. HEADACHE OR FACIAL PAIN ATTRIBUTED TO DISORDER OF CRANIUM, NECK, EYES, EARS, NOSE, SINUSES, TEETH, MOUTH OR OTHER FACIAL OR CRANIAL STRUCTURES 12. HEADACHE ATTRIBUTED TO PSYCHIATRIC DISORDER 

IHS	Diagnosis	ICD-10
6.3.5	Headache attributed to encephalotrigeminal or leptomeningeal angiomatosis (Sturge Weber syndrome) [Q85.8]	G44.811

Diagnostic criteria:

Any new acute headache fulfilling criterion C
Facial angioma, seizures and neuroimaging evidence of meningeal angioma ipsilateral to the facial angioma
Evidence exists of causation by the angiomas
Other causes of headache ruled out by appropriate investigations

Comment:

Headache is commonly reported in this condition but poorly documented. Isolated cases suggest that encephalotrigeminal or leptomeningeal angiomatosis may be a cause of symptomatic migraine, particularly of attacks with prolonged auras (possibly related to chronic oligaemia).

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IHS vs. ICD-10

To facilitate headache diagnosis in daily practice, the classification provides the corresponding WHO ICD-10NA codes for each IHS code.

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